Kawai M, Kihara Y, Hasegawa K, Matsumori A, Sasayama S
Department of Cardiovascular Medicine, Kyoto University Graduate School of Medicine, Japan.
Jpn Circ J. 2000 Aug;64(8):623-6. doi: 10.1253/jcj.64.623.
This paper reports a case of dilated phase in hypertrophic cardiomyopathy with mid-ventricular obstruction. Following the first cardiac catheterization and endomyocardial biopsy, the patient was diagnosed as having hypertrophic cardiomyopathy (HCM) with mid-ventricular obstruction. He had been first diagnosed at the age of 38 years and was subsequently followed for 20 years. Echocardiogram revealed gradually progressive dilatation of the left ventricle, associated with disappearance of the mid-ventricular obstruction. The second cardiac catheterization and endomyocardial biopsy performed at the age of 58 disclosed that the patient was in the dilated phase of HCM with a dip-and-plateau pattern diastolic pressure trace.
本文报告1例伴有心室中部梗阻的肥厚型心肌病扩张期病例。在首次心导管检查和心内膜心肌活检后，该患者被诊断为伴有心室中部梗阻的肥厚型心肌病（HCM）。他最初在38岁时被诊断出该病，随后随访了20年。超声心动图显示左心室逐渐进行性扩张，同时心室中部梗阻消失。58岁时进行的第二次心导管检查和心内膜心肌活检显示，该患者处于HCM扩张期，舒张压曲线呈下斜-平段型。
