Suzuki K, Hasegawa K, Nohara R, Matsumori A, Sasayama S
Department of Cardiovascular Medicine, Graduate School of Medicine, Kyoto University, Japan.
Jpn Circ J. 1999 Feb;63(2):137-40. doi: 10.1253/jcj.63.137.
Hypertrophic cardiomyopathy (HCM) is a disease characterized by an unknown cause of hypertrophy in the left or right ventricle. The dilated phase of HCM shows disease conditions resembling dilated cardiomyopathy, such as ventricular dilation, thin ventricular wall, and reduction of the ejection fraction. A patient presented with left ventricular concentric hypertrophy accompanied by right ventricular dilatation of unknown cause. Right ventricular endomyocardial biopsy specimens showed characteristic myocardial disarray. Therefore, there is the possibility that the patient had right and left ventricular HCM in the process toward the dilated phase, in which dilatation first occurred in the right ventricle.
肥厚型心肌病(HCM)是一种以左心室或右心室不明原因肥厚为特征的疾病。HCM的扩张期表现出类似于扩张型心肌病的病症,如心室扩张、心室壁变薄和射血分数降低。一名患者出现原因不明的左心室向心性肥厚伴右心室扩张。右心室心内膜活检标本显示出特征性的心肌紊乱。因此,该患者有可能在向扩张期发展的过程中同时患有右心室和左心室HCM,其中右心室首先出现扩张。