Yano T, Sawaishi Y, Toyono M, Takaku I, Takada G
Department of Pediatrics; Akita University School of Medicine;, Akita, Japan.
Pediatr Neurol. 2000 Aug;23(2):164-6. doi: 10.1016/s0887-8994(00)00168-5.
Intractable complex partial seizures developed in a 3-year-old female with normal intracranial findings on computed tomography. Frontal paramedian band-like depression of the skin gradually developed thereafter, and progressive facial hemiatrophy (Parry-Romberg syndrome) was diagnosed. Computed tomography scanning at 5 years of age revealed multiple parenchymal calcifications and low-density areas in the white matter of the frontoparietal lobes. Epileptic seizures, one of the major neurologic complications of progressive facial hemiatrophy, could precede the succeeding neurocutaneous changes.
一名3岁女性出现难治性复杂部分性癫痫发作,计算机断层扫描显示颅内情况正常。此后,额部正中旁皮肤逐渐出现带状凹陷,最终被诊断为进行性面部半侧萎缩(帕里-罗姆伯格综合征)。5岁时的计算机断层扫描显示额顶叶白质有多处实质钙化和低密度区。癫痫发作是进行性面部半侧萎缩的主要神经并发症之一,可能先于后续的神经皮肤改变出现。