Székely E, Kulka J, Miklós I, Kaliszky P
Semmelweis University, 2nd Department of Pathology, Budapest, Hungary.
Pathol Oncol Res. 2000;6(3):233-6. doi: 10.1007/BF03032379.
Sarcomas of the great vessels are rare. Altogether 400 such cases have been described in the aorta, the pulmonary artery, and inferior vena cava. The clinical symptoms are generally related to embolic phenomena, aneurysm formation, and widespread metastases, especially to bones. With improved diagnostic modalities more cases are diagnosed and treated surgically. Resection of the tumor may prolong the patient s life. In this paper authors present two cases of such rare sarcomas. In our first case a tumor has developed in the thoracic aorta with symptoms of imminent aortic dissection. The tumorous nature of the lesion was revealed only histologically, since neither the operation, nor macroscopic picture gave any clue to its tumorous nature. The second case was a male patient with a huge retroperitoneal tumor arising from the inferior vena cava, which was clinically suspected to be a carcinomaarising in the adrenal gland.
大血管肉瘤很罕见。主动脉、肺动脉和下腔静脉总共报道过400例此类病例。临床症状通常与栓塞现象、动脉瘤形成和广泛转移有关，尤其是骨转移。随着诊断方法的改进，更多此类病例得以诊断并接受手术治疗。肿瘤切除可延长患者生命。本文作者介绍了两例这种罕见的肉瘤病例。在我们的第一例病例中，胸主动脉出现了一个肿瘤，伴有即将发生主动脉夹层的症状。病变的肿瘤性质仅通过组织学检查得以揭示，因为手术和肉眼观察均未提示其肿瘤性质。第二例病例是一名男性患者，其下腔静脉出现一个巨大的腹膜后肿瘤，临床上怀疑是肾上腺来源的癌。
