Hsu H H, Chen Y C, Fang J T, Huang C C, Shih L Y, Ghuang C K
Division of Nephrology, Department of Medicine, Chang Gung Memorial Hospital, Kweishan, Taoyuan, Taiwan.
Urology. 2000 Nov 1;56(5):856. doi: 10.1016/s0090-4295(00)00783-4.
We describe a patient with an unusual case of unicentric Castleman's disease, which bore a malignant appearance and was located in the pararenal space. She initially presented with hydronephrosis. Two years after surgical removal of the tumor, no recurrence was evident. To our knowledge, only 2 additional cases of this uncommon disease entity associated with hydronephrosis have been reported. Furthermore, our patient was the first to receive conservative surgery. On the basis of our experience, owing to the benign clinical course of this tumor and its excellent response to limited resection, radical surgery may be avoided.
我们描述了一位患有罕见单中心Castleman病的患者，该病例呈现恶性外观，位于肾旁间隙。她最初表现为肾积水。肿瘤手术切除两年后，未见复发迹象。据我们所知，仅有另外2例这种与肾积水相关的罕见疾病实体的病例被报道。此外，我们的患者是首例接受保守手术的。基于我们的经验，由于该肿瘤的临床病程良性且对有限切除反应良好，可避免进行根治性手术。
