Yesil M, Bayata S, Susam I, Dinçkal H, Postaci N
Department of Cardiology, Izmir Ataturk State Hospital, Turkey.
Europace. 1999 Oct;1(4):280-2. doi: 10.1053/eupc.1999.0051.
Although arrhythmias are common in hypertrophic cardiomyopathy (HCM), complete atrioventricular (AV) block is very unusual. A 27-year-old female presented with a recent history of syncope and exercise intolerance. ECG demonstrated complete AV block. Two-dimensional Doppler echocardiography revealed HCM with a 60 mmHg left ventricular outflow tract (LVOT) gradient. A temporary transvenous ventricular pacemaker was inserted urgently, and subsequently replaced by a permanent DDD pacemaker. All symptoms were eliminated. This symptomatic improvement was associated with complete disappearance of LVOT gradient at the time of implantation. No gradient was observed during early follow-up and at 6 months after DDD pacemaker implantation.
虽然心律失常在肥厚型心肌病（HCM）中很常见，但完全性房室传导阻滞却非常罕见。一名27岁女性近期出现晕厥和运动不耐受病史。心电图显示完全性房室传导阻滞。二维多普勒超声心动图显示为肥厚型心肌病，左心室流出道（LVOT）压差为60 mmHg。紧急插入了临时经静脉心室起搏器，随后更换为永久性DDD起搏器。所有症状均消失。这种症状改善与植入时LVOT压差完全消失有关。在DDD起搏器植入后的早期随访及6个月时均未观察到压差。
