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肥厚型心肌病伴三度房室传导阻滞。

Hypertrophic cardiomyopathy presenting with 3rd-degree atrioventricular block.

作者信息

Rosen K L, Cameron R W, Bigham P J, Neish S R

机构信息

Department of Pediatrics, Fitzsimons Army Medical Center, Aurora, Colorado 80045, USA.

出版信息

Tex Heart Inst J. 1997;24(4):372-5.

PMID:9456495
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC325485/
Abstract

A 15-year-old boy presented with exercise intolerance and near syncope. Electrocardiography showed 3rd-degree atrioventricular block. He was treated emergently with temporary transvenous ventricular pacing. Two-dimensional echocardiography revealed hypertrophic cardiomyopathy. Subsequently, a permanent, transvenous, dual-chamber pacemaker was implanted. Hypertrophic cardiomyopathy rarely causes complete atrioventricular block. It is particularly unusual for the presenting symptoms of hypertrophic cardiomyopathy to be caused by atrioventricular block. The case report is followed by a review of the pediatric literature on hypertrophic cardiomyopathy with atrioventricular block.

摘要

一名15岁男孩出现运动不耐受和接近晕厥的症状。心电图显示三度房室传导阻滞。他接受了紧急临时经静脉心室起搏治疗。二维超声心动图显示肥厚型心肌病。随后,植入了永久性经静脉双腔起搏器。肥厚型心肌病很少导致完全性房室传导阻滞。肥厚型心肌病以房室传导阻滞为首发症状尤其罕见。病例报告之后是对小儿肥厚型心肌病合并房室传导阻滞相关文献的综述。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b494/325485/8a29dfd998b3/thij00027-0143-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b494/325485/86b3d96a196c/thij00027-0143-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b494/325485/8a29dfd998b3/thij00027-0143-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b494/325485/86b3d96a196c/thij00027-0143-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b494/325485/8a29dfd998b3/thij00027-0143-b.jpg

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1
Hypertrophic cardiomyopathy presenting with 3rd-degree atrioventricular block.肥厚型心肌病伴三度房室传导阻滞。
Tex Heart Inst J. 1997;24(4):372-5.
2
Rare association of hypertrophic cardiomyopathy and complete atrioventricular block with prompt disappearance of outflow gradient after DDD pacing.肥厚型心肌病与完全性房室传导阻滞的罕见关联,以及DDD起搏后流出道梯度迅速消失。
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Complete Heart Block in Hypertrophic Cardiomyopathy: A Rare Association.肥厚型心肌病中的完全性心脏传导阻滞:一种罕见的关联。
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引用本文的文献

1
An Unusual Presentation of Third-Degree Atrioventricular Block in a Patient With Hypertrophic Cardiomyopathy.肥厚型心肌病患者三度房室传导阻滞的不寻常表现。
Cureus. 2025 Jul 30;17(7):e89041. doi: 10.7759/cureus.89041. eCollection 2025 Jul.
2
Cardiac Magnetic Resonance Identified the Fibrotic Lesion Associated with Syncope Attack Due to Complete Atrioventricular Block in a Patient with Hypertrophic Cardiomyopathy and Aortic Stenosis.心脏磁共振成像识别出肥厚型心肌病和主动脉瓣狭窄患者因完全性房室传导阻滞导致晕厥发作相关的纤维化病变。
Intern Med. 2019 Jul 15;58(14):2041-2044. doi: 10.2169/internalmedicine.2563-18. Epub 2019 Mar 28.
3

本文引用的文献

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Abrupt aggravation of atrioventricular block and syncope in hypertrophic cardiomyopathy.肥厚型心肌病患者房室传导阻滞及晕厥的突然加重
Arch Dis Child. 1995 Dec;73(6):536-7. doi: 10.1136/adc.73.6.536.
2
Prognostic significance of 24 hour ambulatory electrocardiographic monitoring in patients with hypertrophic cardiomyopathy: a prospective study.24小时动态心电图监测对肥厚型心肌病患者的预后意义:一项前瞻性研究
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Hypertrophic cardiomyopathy complicated by complete heart block. Case report and review of the literature.
S Afr Med J. 1984 Dec 1;66(22):847-55.
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Chic Med Sch Q. 1965 Fall;25(3):169-75.
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Hypertrophic obstructive cardiomyopathy associated with complete heart block. Pathologic correlations in a case studied with His bundle electrography.肥厚性梗阻性心肌病合并完全性心脏传导阻滞。希氏束电图研究病例的病理相关性。
Acta Cardiol. 1974;29(3):241-9.
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Familial spontaneous complete heart block in hypertrophic cardiomyopathy.肥厚型心肌病中的家族性自发性完全性心脏传导阻滞。
Br Heart J. 1986 May;55(5):469-74. doi: 10.1136/hrt.55.5.469.
9
Arrhythmia and prognosis in infants, children and adolescents with hypertrophic cardiomyopathy.肥厚型心肌病婴幼儿、儿童及青少年的心律失常与预后
J Am Coll Cardiol. 1988 Jan;11(1):147-53. doi: 10.1016/0735-1097(88)90181-7.
10
Familial hypertrophic cardiomyopathy associated with spontaneous complete heart block.家族性肥厚型心肌病合并自发性完全性心脏传导阻滞。
J Med Assoc Thai. 1991 Jul;74(7):301-5.