Tokunaga S, Kado H, Imoto Y, Shiokawa Y, Yasui H
Department of Cardiovascular Surgery, Fukuoka Children's Hospital, Japan.
Ann Thorac Surg. 2001 Feb;71(2):715-7. doi: 10.1016/s0003-4975(00)02224-4.
Ectopia cordis is a very rare and often fatal disease. We report a successful surgery case of thoracoabdominal ectopia cordis with univentricular heart. This patient underwent a three-stage Fontan procedure, a right-modified Blalock-Taussig shunt at the age of 1 month, bidirectional Glenn shunt and pulmonary arterioplasty at 2 years 8 months, and finally a total cavopulmonary connection at 4 years. This patient was discharged from the hospital in good condition and has been doing well since. Thus, ectopia cordis is not a contraindication for a Fontan operation.
心脏异位是一种非常罕见且通常致命的疾病。我们报告一例胸腹型心脏异位合并单心室的成功手术病例。该患者接受了三阶段的Fontan手术，1个月大时进行了右改良Blalock-Taussig分流术，2岁8个月时进行了双向Glenn分流术和肺动脉成形术，最后在4岁时进行了全腔静脉肺动脉连接术。该患者康复出院，此后情况良好。因此，心脏异位并非Fontan手术的禁忌证。
