Marino Amy L, Levy Richard J, Berger John T, Donofrio Mary T
Division of Cardiology, Children's National Medical Center, Washington, DC, USA.
Pediatr Cardiol. 2011 Apr;32(4):498-502. doi: 10.1007/s00246-010-9867-6. Epub 2011 Jan 6.
We present a case of ectopia cordis with a complex single-ventricle congenital heart defect in association with pentalogy of Cantrell. Management by a skilled multidisciplinary team was critical for patient survival. Early fetal diagnosis and the use of advanced imaging techniques allowed adequate time for planning and identified critical anatomic details. Preserving the heart's natural covering, performing cardiac surgery without cardiopulmonary bypass, and using catheter intervention decreased the risk to the patient. Complete coverage of the defect was achieved using skin generated with tissue expanders. This case illustrates the importance of collaboration when caring for infants with critical, high-risk disease and highlights the increased potential for survival with complex ectopia cordis in the current medical era.
我们报告一例合并Cantrell五联症的心脏异位并伴有复杂单心室先天性心脏缺陷的病例。由技术娴熟的多学科团队进行管理对患者存活至关重要。早期胎儿诊断以及先进成像技术的应用为规划提供了充足时间，并明确了关键的解剖细节。保留心脏的天然包膜、在无体外循环的情况下进行心脏手术以及采用导管介入降低了患者风险。使用组织扩张器生成的皮肤实现了缺损的完全覆盖。该病例说明了在护理患有严重高危疾病的婴儿时协作的重要性，并凸显了在当前医学时代复杂心脏异位患者存活可能性的增加。
