Rygl M, Snajdauf J, Pýcha K, Morávek J, Kodet R, Vondrichová H
Klinika dĕtské chirurgie 2. LF UK a FN Motol, Praha.
Rozhl Chir. 2000 Dec;79(12):609-12.
The authors evaluate their experience with the diagnosis and treatment of abdominal lymphangiomas during the period of 1995-1999. During the above period 6 girls and 4 boys with abdominal lymphangiomas were operated. The mean age at the time of operation was 5 years and 8 months. Ultrasonographic examination was made in all 10 patients, CT examination in 8. The surgical finding was lymphangioma of the mesenterium 4x, of the omentum 2x, of the adrenals 2x of the retroperitoneum 1x and intestinal lymphangiomatosis 1x. Macroscopically complete extirpation of the lymphangioma was possible in 9 patients and called for resection of the gut 3x and for adrenalectomy 2x. In one patient subtotal extirpation was performed. Postoperative follow-up did not reveal a relapse in any of the children. Abdominal cystic lymphangiomas are rare benign malformations of the lymphatic system. For preoperative differential diagnosis in typical cases USG is sufficient. The therapeutic method is complete surgical extirpation which is associated with a low incidence of relapses.
作者评估了他们在1995年至1999年期间对腹部淋巴管瘤的诊断和治疗经验。在上述期间，对6名患有腹部淋巴管瘤的女孩和4名男孩进行了手术。手术时的平均年龄为5岁8个月。所有10例患者均进行了超声检查，8例进行了CT检查。手术发现肠系膜淋巴管瘤4例，大网膜淋巴管瘤2例，肾上腺淋巴管瘤2例，腹膜后淋巴管瘤1例，肠淋巴管瘤病1例。9例患者在宏观上能够完全切除淋巴管瘤，其中3例需要切除肠道，2例需要进行肾上腺切除术。1例患者进行了次全切除。术后随访未发现任何儿童复发。腹部囊性淋巴管瘤是淋巴系统罕见的良性畸形。对于典型病例，术前超声检查足以进行鉴别诊断。治疗方法是完全手术切除，复发率较低。
