Laster Z, Temkin D, Zarfin Y, Kushnir A
Department of Oral and Maxillofacial Surgery, Poriya Hospital, Tiberias, Israel.
Int J Oral Maxillofac Surg. 2001 Feb;30(1):75-9. doi: 10.1054/ijom.2000.0009.
Congenital craniofacial disorders represent approximately 20% of all birth defects. One of these disorders is syngnathia, of which only 24 cases have been reported since 1936. Twenty cases involved fusion of the alveolar processes of the maxilla and mandible. Only four are similar to the presented case, which includes bony fusion of the ascending ramus of the mandible to the zygomatic complex and the posterior part of the maxilla. This case report will present details from the 23rd week of gestation to 8 months of age when the infant underwent the first attempt to free the syngnathia. The literature is discussed and a causative mechanism and new classification are proposed.
先天性颅面疾病约占所有出生缺陷的20%。其中一种疾病是并颌畸形,自1936年以来仅报告了24例。20例涉及上颌骨和下颌骨牙槽突融合。只有4例与本病例相似,包括下颌骨升支与颧骨复合体及上颌骨后部的骨性融合。本病例报告将呈现从妊娠第23周直至婴儿8个月大时首次尝试松解并颌畸形的详细情况。文中对相关文献进行了讨论,并提出了一种致病机制和新的分类方法。