Froehner M, Gaertner H J, Hakenberg O W, Wirth M P
Department of Urology, University Clinics Carl Gustav Carus, Technical University of Dresden, Germany.
Surg Today. 2001;31(3):242-5. doi: 10.1007/s005950170177.
Sarcomas rarely arise in the intestinum, and leiomyosarcoma represents the majority of cases. With only seven cases reported in the available English literature up to now, malignant fibrous histiocytoma of the small intestine is exceedingly rare. Moreover, follow-up data are almost completely unavailable. We present herein the unique case of a malignant fibrous histiocytoma arising in a postoperatively adherent intestinal loop. To the best of our knowledge, this is the first such case ever to be described. The clinical history and the intraoperative findings suggested that chronic postoperative repair processes might have been a promoting factor in the tumorigenesis of this neoplasm, on the analogy of malignant fibrous histiocytoma arising at different sites. The patient recovered well but 9.5 years after surgical removal, a solitary recurrent tumor developed in the urinary bladder and progressed rapidly, highlighting the need for long-term, possibly life-long, surveillance of patients with this rare type of intestinal cancer.
肉瘤很少发生于肠道，其中平滑肌肉瘤占大多数病例。截至目前，英文文献中仅报道过7例小肠恶性纤维组织细胞瘤，极为罕见。此外，几乎没有随访数据。在此，我们报告一例发生于术后粘连肠袢的恶性纤维组织细胞瘤的独特病例。据我们所知，这是首例此类病例的描述。临床病史和术中发现提示，术后慢性修复过程可能是该肿瘤发生的促发因素，类似于不同部位发生的恶性纤维组织细胞瘤。患者恢复良好，但手术切除9.5年后，膀胱出现孤立性复发性肿瘤且进展迅速，这凸显了对这种罕见类型的肠道癌患者进行长期甚至可能终身监测的必要性。
