Kallinen J, Marin K, Heinonen S, Mannermaa A, Palotie A, Ryynänen M
Department of Obstetrics and Gynaecology, University Hospital of Kuopio, Finland.
BJOG. 2001 May;108(5):505-9. doi: 10.1111/j.1471-0528.2001.00118.x.
To investigate the applicability of carrier screening in women undergoing invasive prenatal diagnosis.
Prospective study.
University-based clinic.
Two hundred and fifty-six pregnant women.
Gene tests were offered for fragile X syndrome, aspartylglycosaminuria and infantile neuronal ceroid lipofuscinosis at the time of invasive prenatal testing.
The overall uptake of the tests was 92%. Previously unrecognised carriership was found in 10 women: aspartylglycosaminuria (7); infantile neuronal ceroid lipofuscinosis (2) and fragile X (1). Fetal genotyping was carried out in one carrier of aspartylglycosaminuria whose partner was also a carrier, and in one woman who was found to have fragile X premutation. Both fetuses were unaffected.
Carrier screening for single-gene disorders is feasible and well accepted among pregnant women undergoing invasive prenatal testing. The major benefit is that there is no need to consider extra invasive tests when carriership is detected. Incorporation of genetic testing into fetal karyotyping gives more security to future parents.
探讨携带者筛查在接受侵入性产前诊断的女性中的适用性。
前瞻性研究。
大学附属医院诊所。
256名孕妇。
在进行侵入性产前检测时,对脆性X综合征、天冬氨酰氨基葡糖苷尿症和婴儿型神经元蜡样脂褐质沉积症进行基因检测。
检测的总体接受率为92%。在10名女性中发现了此前未被识别的携带者状态:天冬氨酰氨基葡糖苷尿症(7例);婴儿型神经元蜡样脂褐质沉积症(2例)和脆性X综合征(1例)。对1名天冬氨酰氨基葡糖苷尿症携带者且其伴侣也是携带者的孕妇以及1名被发现有脆性X前突变的女性进行了胎儿基因分型。两个胎儿均未受影响。
对单基因疾病进行携带者筛查是可行的,并且在接受侵入性产前检测的孕妇中得到了很好的接受。主要益处在于,当检测到携带者状态时无需考虑额外的侵入性检测。将基因检测纳入胎儿核型分析可为准父母提供更多保障。