Ripari M, Cicconetti A, Sed M, Maggiore C
Cattedra di Clinica Odontostomatologica, Università degli Studi La Sapienza, Rome, Italy.
Minerva Stomatol. 2001 Jun;50(6):229-32.
Gardner's syndrome is a congenital condition characterised by diffuse intestinal adenomatous polyposis (IAP) associated with maxillary osteomas, odontomas, hypertrophy of the retinal epithelium and skin tumours. It may affect subjects of all ages with equal frequency in males and females. The fact that diffuse adenomatous polyposis, the most serious clinical aspect of the syndrome, is treated surgically, has led to improved survival in patients and, consequently, an increased incidence in associated lesions, particularly maxillary osteomas. A personal case observed at the Odontostoma-tological Clinic of the University of Rome La Sapienza is reported.
加德纳综合征是一种先天性疾病，其特征为弥漫性肠道腺瘤性息肉病（IAP），伴有上颌骨瘤、牙瘤、视网膜上皮肥大和皮肤肿瘤。它可在所有年龄段的男性和女性中以相同频率发病。该综合征最严重的临床方面——弥漫性腺瘤性息肉病通过手术治疗，这使得患者的生存率提高，进而导致相关病变尤其是上颌骨瘤的发病率增加。本文报告了在罗马第一大学牙瘤病诊所观察到的一例个人病例。
