Butterworth J
J Inherit Metab Dis. 1978;1(1):25-8. doi: 10.1007/BF01805711.
Assay of alpha-L-iduronidase, heparin sulphamidase, N-acetyl-alpha-D-glucosaminidase, arylsulphatase B, alpha-L-fucosidase, beta-glucuronidase, beta-galactosidase and alpha-D-mannosidase in cultured cells is described. Activities in deficient fibroblast strains are compared to control fibroblast strains. The first case of Sanfilippo B in the United Kingdom is reported. A comparison of enzyme activities in cultured fibroblasts and amniotic fluid cells is made.
描述了在培养细胞中对α-L-艾杜糖醛酸酶、硫酸乙酰肝素酶、N-乙酰-α-D-氨基葡萄糖苷酶、芳基硫酸酯酶B、α-L-岩藻糖苷酶、β-葡萄糖醛酸酶、β-半乳糖苷酶和α-D-甘露糖苷酶的测定。将缺陷型成纤维细胞系中的活性与对照成纤维细胞系进行比较。报告了英国首例桑菲利波B病病例。对培养的成纤维细胞和羊水细胞中的酶活性进行了比较。