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The enzymes of the hepatic phenylalanine hydroxylating system.

作者信息

Kaufman S

出版信息

J Inherit Metab Dis. 1978;1(2):63-5. doi: 10.1007/BF01801846.

DOI:10.1007/BF01801846
PMID:117244
Abstract
摘要

相似文献

1
The enzymes of the hepatic phenylalanine hydroxylating system.
J Inherit Metab Dis. 1978;1(2):63-5. doi: 10.1007/BF01801846.
2
Atypical phenylketonuria with normal phenylalanine hydroxylase and dihydropteridine reductase activity in vitro.体外苯丙氨酸羟化酶和二氢蝶啶还原酶活性正常的非典型苯丙酮尿症。
Pediatrics. 1977 May;59(5):757-61.
3
The implications of multiple forms of phenylalanine hydroxylase in phenylketonuria and related diseases of phenylalanine metabolism.苯丙酮尿症及苯丙氨酸代谢相关疾病中多种形式苯丙氨酸羟化酶的意义。
Biochem Med. 1976 Feb;15(1):55-86. doi: 10.1016/0006-2944(76)90074-0.
4
[Comparative effects of different inhibitors of phenylalanine hydroxylase and dihydropteridine reductase. In vivo and in vitro study in rats].[苯丙氨酸羟化酶和二氢蝶啶还原酶不同抑制剂的比较作用。大鼠体内和体外研究]
Arch Fr Pediatr. 1978 Dec;35(10 Suppl):93-101.
5
Enzymology of the phenylalanine-hydroxylating system.
Enzyme. 1987;38(1-4):286-95. doi: 10.1159/000469218.
6
[Phenylalanine hydroxylase activity in the liver as a parameter for distinguishing various forms of hyperphenylalaninemias (author's transl)].
Clin Chim Acta. 1975 Jan 6;58(1):17-21. doi: 10.1016/0009-8981(75)90480-5.
7
Nature of the molecular defect in phenylketonuria and hyperphenylalaninaemia.
Nature. 1972 Nov 17;240(5377):157-9. doi: 10.1038/240157a0.
8
Biopterins in arginase, dihydropteridine reductase and phenylalanine hydroxylase deficiency.精氨酸酶、二氢蝶啶还原酶和苯丙氨酸羟化酶缺乏症中的生物蝶呤
J Neurol Neurosurg Psychiatry. 1987 Feb;50(2):242. doi: 10.1136/jnnp.50.2.242.
9
Hepatic phenylalanine hydroxylase activity in hyperphenylalaninaemia.高苯丙氨酸血症患者的肝脏苯丙氨酸羟化酶活性
J Inherit Metab Dis. 1981;4(2):59-60. doi: 10.1007/BF02263590.
10
[The phenylalanine hydroxylase system].[苯丙氨酸羟化酶系统]
Arch Fr Pediatr. 1983;40 Suppl 1:219-21.

引用本文的文献

1
Hyperphenylalaninaemia of various types among three-quarters of a million neonates tested in a screening programme.在一项筛查项目中对75万新生儿进行检测，发现了各种类型的高苯丙氨酸血症。
Arch Dis Child. 1981 Oct;56(10):759-64. doi: 10.1136/adc.56.10.759.

本文引用的文献

1
Pteridine cofactors.蝶啶辅因子
Annu Rev Biochem. 1967;36:171-84. doi: 10.1146/annurev.bi.36.070167.001131.
2
Studies on the mechanism of the enzymatic conversion of phenylalanine to tyrosine.苯丙氨酸向酪氨酸酶促转化机制的研究。
J Biol Chem. 1959 Oct;234:2677-82.
3
STUDIES ON THE STRUCTURE OF THE PRIMARY OXIDATION PRODUCT FORMED FROM TETRAHYDROPTERIDINES DURING PHENYLALAMINE HYDROXYLATION.苯丙氨酸羟化过程中四氢蝶啶形成的初级氧化产物结构研究。
J Biol Chem. 1964 Jan;239:332-8.
4
THE STRUCTURE OF THE PHENYLALANINE-HYDROXYLATION COFACTOR.苯丙氨酸羟化酶辅因子的结构
Proc Natl Acad Sci U S A. 1963 Dec;50(6):1085-93. doi: 10.1073/pnas.50.6.1085.
5
Purification and some physical properties of phenylalanine hydroxylase from rat liver.大鼠肝脏苯丙氨酸羟化酶的纯化及某些物理性质
J Biol Chem. 1970 Sep 25;245(18):4745-50.
6
Phenylalanine hydroxylase of human liver: assay and some properties.人肝脏苯丙氨酸羟化酶：测定方法及某些性质
Arch Biochem Biophys. 1969 Oct;134(1):249-52. doi: 10.1016/0003-9861(69)90273-2.
7
Ontogenesis of phenylalanine and tryptophan hydroxylation in rat brain and liver.大鼠脑和肝脏中苯丙氨酸和色氨酸羟化作用的个体发生
Biol Neonate. 1971;18(1):85-93. doi: 10.1159/000240350.
8
Detection of hepatic phenylalanine 4-hydroxylase in classical phenylketonuria.经典型苯丙酮尿症中肝脏苯丙氨酸4-羟化酶的检测
Proc Natl Acad Sci U S A. 1973 Feb;70(2):552-6. doi: 10.1073/pnas.70.2.552.
9
The isolation and characterization of dihydropteridine reductase from sheep liver.绵羊肝脏中二氢蝶啶还原酶的分离与鉴定
J Biol Chem. 1972 Oct 10;247(19):6082-91.
10
Partial purification and characterization of tryptophan hydroxylase from rabbit hindbrain.兔后脑色氨酸羟化酶的部分纯化及特性分析
J Biol Chem. 1972 Jul 10;247(13):4165-73.