Jacq L, Lupoglazoff J M, Magnier S, Vouhe P, Casasoprana A
Service de cardiologie infantile, hôpital Robert-Debré, 48, boulevard Serrurier, 75019 Paris.
Arch Mal Coeur Vaiss. 2001 Oct;94(10):1123-6.
The authors report the case of a 15 month-old infant admitted to the intensive care unit for cardiogenic shock due to rupture of an aneurysm of the right anterior sinus of Valsalva into the left ventricle, associated with massive aortic regurgitation. The patient underwent a Ross procedure with resection of the aneurysm. This is a very rare condition because rupture of the aneurysm into the left ventricle has not been previously reported in a young girl to the best of the authors' knowledge. Moreover, a Ross procedure has not been previously described in this indication. The case illustrates the diagnostic difficulty associated with this pathology and underlines the necessity of thinking of this diagnosis in infants with appearances of dilated cardiomyopathy and aortic regurgitation.
作者报告了一例15个月大的婴儿,因瓦尔萨尔瓦窦右前窦动脉瘤破裂进入左心室并伴有大量主动脉反流而导致心源性休克,被收入重症监护病房。该患者接受了Ross手术并切除了动脉瘤。这是一种非常罕见的情况,据作者所知,此前尚未有年轻女孩出现动脉瘤破裂进入左心室的报道。此外,此前也没有关于该适应症的Ross手术的描述。该病例说明了与这种病理相关的诊断困难,并强调了在出现扩张型心肌病和主动脉反流的婴儿中考虑这种诊断的必要性。