Mair D D, Fulton R E, McGoon D C
Mayo Clin Proc. 1975 Dec;50(12):691-6.
Aortico-left ventricular tunnel is a rare congenital malformation in which a perivalvular tunnel produces free communication between the aortic root and left ventricle. The hemodynamic consequences of this lesion are similar to those of aortic valve incompetence. Infants with this condition have clinical findings that should suggest it as a diagnostic possibility, and aortic root angiocardiography can establish the diagnosis. Early severe congestive heart failure is common in infants with this malformation, and in such patients prompt surgical correction of the deformity is recommended. This paper reports surgical correction of aortico-left ventricular tunnel in a 9-month-old child, the first reported patient to be successfully operated on before age 2 years.
主动脉-左心室通道是一种罕见的先天性畸形，其中瓣膜周围通道使主动脉根部与左心室之间形成自由交通。该病变的血流动力学后果与主动脉瓣关闭不全相似。患有这种疾病的婴儿具有一些临床特征，这些特征提示应将其作为一种诊断可能性，主动脉根部血管造影可以确诊。早期严重充血性心力衰竭在患有这种畸形的婴儿中很常见，对于这类患者，建议及时进行手术矫正畸形。本文报告了一名9个月大儿童的主动脉-左心室通道手术矫正情况，该患儿是首例报道的2岁前成功接受手术的患者。
