Matthews J J, Roberts R, O'Reilly D A, Schick S, Kingsnorth A N
Department of Surgery, Derriford Hospital, Plymouth, UK.
Dig Surg. 2002;19(1):65-6. doi: 10.1159/000052010.
A 64-year-old man with Muir-Torre syndrome (MTS), a condition characterized by the association of multiple sebaceous tumours and kerato-acanthomas with internal malignancies, developed a carcinoma of the ampulla of Vater. This is the 2nd reported ampullary carcinoma in 205 reported cases of MTS, suggesting a higher prevalence in MTS patients than in the general population. As an ampullary carcinoma is potentially amenable to surgical resection, particularly when detected early, patients with MTS should undergo regular endoscopic surveillance of the ampulla of Vater.
一名64岁患有穆尔-托雷综合征（MTS）的男性，该病症的特征是多发性皮脂腺肿瘤和角化棘皮瘤与内部恶性肿瘤相关联，他患上了 Vater壶腹癌。这是在205例报告的MTS病例中第2例报告的壶腹癌，表明MTS患者的患病率高于普通人群。由于壶腹癌有可能通过手术切除，特别是在早期发现时，MTS患者应定期接受Vater壶腹的内镜监测。
