Akay Kamil Melih, Izci Yusuf, Baysefer Alper
Department of Neurosurgery, Gulhane Military Medical Academy, Ankara, Turkey.
Pediatr Neurosurg. 2002 May;36(5):225-8. doi: 10.1159/000058424.
Split cord malformations (SCMs) are rare spinal anomalies and their classification is still a matter of debate. There is no widespread consensus on the embryological basis of this entity. The unified theory, proposed by Pang et al. [Neurosurgery 1992;31:451-480], was an attempt to explain the embryogenetic mechanism as a basic error occurring around the time when the primitive neuroenteric canal closes. We report two unusual cases of SCMs with a dorsally situated bony spur. We analyzed the radiological, clinical and surgical features of the lesions and were not able to classify these cases according to the unified theory. Further embryological studies should be conducted to elucidate the mechanisms of occurrence of these lesions, and the dorsal bony septum variant should be considered in SCM surgery.
脊髓纵裂畸形(SCMs)是罕见的脊柱异常,其分类仍存在争议。对于该实体的胚胎学基础尚未达成广泛共识。Pang等人[《神经外科学》1992年;31:451 - 480]提出的统一理论试图将胚胎发生机制解释为原始神经肠管闭合时发生的基本错误。我们报告了两例伴有背侧骨棘的不寻常脊髓纵裂畸形病例。我们分析了病变的放射学、临床和手术特征,无法根据统一理论对这些病例进行分类。应进行进一步的胚胎学研究以阐明这些病变的发生机制,并且在脊髓纵裂畸形手术中应考虑背侧骨隔变异情况。