中间型脊髓纵裂畸形：假说与病例报告。

The intermediate type split cord malformation: hypothesis and case report.

作者信息

van Aalst J, Beuls E A M, Vles J S H, Cornips E M J, van Straaten H W M

机构信息

Department of Neurosurgery, University Hospital Maastricht, P. Debyelaan 25, P. O. Box 5800, 6202 AZ, Maastricht, The Netherlands.

出版信息

Childs Nerv Syst. 2005 Dec;21(12):1020-4. doi: 10.1007/s00381-005-1159-8. Epub 2005 Apr 29.

DOI:10.1007/s00381-005-1159-8

PMID:15864598

Abstract

METHODS

A patient is described in which a complete osteofibrotic dorsally implanted septum was found in combination with a split cord malformation in a single dural tube. This case cannot be explained using the widely used theory as proposed by Pang et al. [Pang D, Dias MS, Ahab-Barmada M (1992) Split cord malformation, part I: A unified theory of embryogenesis for double spinal cord malformations. Neurosurgery 31:451-480] but must be regarded as a combination of type I and II split cord malformation.

RESULTS

The authors state that all types of split cord malformation can be reduced to a single derailment during development, with various degrees of severity.

CONCLUSIONS

The configuration of the malformation is determined by the way the median parts of the mesoderm come to development. Type I and II split cord malformation are not distinct entities.

摘要

方法

描述了一名患者，其背侧植入的中隔完全骨化纤维化，并伴有单一硬脊膜管内的脊髓纵裂畸形。该病例无法用Pang等人提出的广泛应用的理论来解释[Pang D, Dias MS, Ahab-Barmada M(1992)脊髓纵裂畸形，第一部分：双脊髓畸形胚胎发生的统一理论。神经外科学31:451 - 480]，而必须被视为I型和II型脊髓纵裂畸形的组合。