Laufer Marc R
Curr Opin Obstet Gynecol. 2002 Oct;14(5):441-4. doi: 10.1097/00001703-200210000-00001.
To review the Mayer-von Rokitansky-Küster-Hauser syndrome and to address means of diagnosis, patient education and counselling. The timing of, and vast options for, creation of a functional vaginal are also discussed.
The diagnosis of Mayer-von Rokitansky-Küster-Hauser usually occurs during an evaluation of primary amenorrhea. Counselling and support are of great importance for affected young women and their families. Educational materials have increased with the availability of Internet web sites and there is a vast number of options for creation of a functional vagina; most international centers promote the utilization of vaginal dilators.
Young girls, adolescents and women with Mayer-von Rokitansky-Küster-Hauser should be offered a comprehensive evaluation, and presented with information regarding all options for management and support. Ongoing psycho-social and educational support is extremely important. International centers that focus on congenital anomalies of the reproductive tract should be developed. These centers of excellence will facilitate long-term follow up studies to improve patient care and evidence based medical options.
回顾迈耶-冯-罗基坦斯基-库斯特-豪泽综合征，并探讨诊断方法、患者教育及咨询。还讨论了构建功能性阴道的时机及众多选择。
迈耶-冯-罗基坦斯基-库斯特-豪泽综合征的诊断通常在原发性闭经评估期间进行。咨询和支持对受影响的年轻女性及其家庭极为重要。随着互联网网站的普及，教育资料有所增加，构建功能性阴道有众多选择；大多数国际中心提倡使用阴道扩张器。
对于患有迈耶-冯-罗基坦斯基-库斯特-豪泽综合征的年轻女孩、青少年和女性，应提供全面评估，并告知她们所有管理和支持的选择。持续的心理社会和教育支持极其重要。应建立专注于生殖道先天性异常的国际中心。这些卓越中心将有助于开展长期随访研究，以改善患者护理及循证医学选择。
