Lee Yu Chang, Chueng Yao Chung, Hsu Shin Wei, Lui Chun Chung
Division of Neuroradiology, Department of Diagnostic Radiology, Chang Gung Memorial Hospital, Kaohsiung, Taiwan.
AJNR Am J Neuroradiol. 2003 Jan;24(1):119-23.
Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is made immediately with biopsy and the involved dura is removed surgically. Consequently, extensive preoperative imaging studies usually are not available. We reviewed a case of idiopathic hypertrophic cranial pachymeningitis and collectively summarized the interesting features from the 7 years preceding surgical treatment. These chronologic imaging findings with progressive intracranial involvement included dural thickening, dural mass, sinus thrombosis, and venous congestion constituted comprehensive pictures of idiopathic hypertrophic cranial pachymeningitis. The thickened dura may also at times mimic dural masses, such as en plaque meningioma.
特发性肥厚性硬脑膜炎是一种罕见的炎症性疾病，硬脑膜呈弥漫性受累。通常，通过活检可立即做出明确诊断，并通过手术切除受累的硬脑膜。因此，术前通常无法获得广泛的影像学研究。我们回顾了一例特发性肥厚性硬脑膜炎病例，并总结了手术治疗前7年的有趣特征。这些颅内进行性受累的按时间顺序排列的影像学表现包括硬脑膜增厚、硬脑膜肿块、窦血栓形成和静脉淤血，构成了特发性肥厚性硬脑膜炎的综合影像。增厚的硬脑膜有时也可能类似硬脑膜肿块，如斑块状脑膜瘤。
