Goyal M, Malik A, Mishra N K, Gaikwad S B
Department of Neuroradiology, All India Institute of Medical Sciences, New Delhi, India.
Neuroradiology. 1997 Sep;39(9):619-23. doi: 10.1007/s002340050479.
Hypertrophic pachymeningitis is extremely rare. It is a fibrosing inflammatory process which involves the dura mater, including the tentorium. Numerous pathological entities produce thickening of the pachymeninges, so that idiopathic hypertrophic pachymeningitis is a diagnosis of exclusion. We describe four patients with idiopathic hypertrophic pachymeningitis who had varied clinical presentation. Imaging studies revealed diffuse thickening of the pachymeninges; in one patient there was extensive dural sinus thrombosis. Since no identifiable cause was found, the cases were labelled as idiopathic.
肥厚性硬脑膜炎极为罕见。它是一种纤维化炎症过程，累及硬脑膜，包括小脑幕。许多病理实体可导致硬脑膜增厚，因此特发性肥厚性硬脑膜炎是一种排除性诊断。我们描述了4例临床表现各异的特发性肥厚性硬脑膜炎患者。影像学研究显示硬脑膜弥漫性增厚；1例患者存在广泛的硬脑膜窦血栓形成。由于未发现可识别的病因，这些病例被诊断为特发性。
