Marcelletti C, McGoon D C, Mair D D
Circulation. 1976 Jul;54(1):108-11. doi: 10.1161/01.cir.54.1.108.
The cases of 23 patients whose condition was diagnosed as truncus arteriosus, type I or II, and who were seen at the Mayo Clinic during the decade preceding 1967, that is, before corrective operation became feasible, were reviewed. Ten were infants (through one year of age), and all ten have died. Eight ranged in age from more than one year through seven years of age, and all are living, except one, who diet 11 years after diagnosis. Five were older than seven years, and all had severe pulmonary vascular obstructive disease; three have died. Thus, 14 of the 23 have died, and all but one surviving patient have mild to moderate disability. The generally grave prognosis for patients with truncus arteriosus warrants continued use of corrective operation, but suggests that the greatest benefit can be realized by successful correction in the infant with congestive heart failure and in early childhood before the development of severe pulmonary vascular obstructive disease.
回顾了1967年前十年间在梅奥诊所就诊的23例被诊断为I型或II型共同动脉干的患者病例，即在此之前矫正手术尚不可行的时候。其中10例为婴儿（一岁及以下），这10例均已死亡。8例年龄在一岁以上至七岁之间，除1例在诊断后11年死亡外，其余均存活。5例年龄大于七岁，均患有严重的肺血管阻塞性疾病；3例已死亡。因此，23例中有14例死亡，除1例存活患者外，其余存活患者均有轻度至中度残疾。共同动脉干患者总体预后不佳，这使得矫正手术仍需继续应用，但表明通过对患有充血性心力衰竭的婴儿以及在严重肺血管阻塞性疾病发展之前的幼儿期成功进行矫正，可获得最大益处。
