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反射性心血管晕厥的一种罕见病因:迷走神经副神经节瘤。

An unusual cause of reflex cardiovascular syncope: vagal paraganglioma.

作者信息

Okmen Ertan, Erdinler Izzet, Oguz Enis, Akyol Ahmet, Cam Nese

机构信息

Department of Cardiology, Siyami Ersek Cardiovascular and Thoracic Surgery Center, Istanbul, Turkey.

出版信息

Ann Noninvasive Electrocardiol. 2003 Apr;8(2):173-6. doi: 10.1046/j.1542-474x.2003.08215.x.

DOI:10.1046/j.1542-474x.2003.08215.x
PMID:12848802
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6932380/
Abstract

Vagal paraganglioma is one of the rare tumors of the neuroendocrine system. We are reporting a vagal paraganglioma case presented with uncommon features of the disease: asystole and syncope. Syncope episodes occurred 3 years before the major symptoms of the disease. Dual chamber pacemaker failed to prevent syncope attacks because of the vasodepressor component. The patient was treated successfully with en bloc removal of tumor and vagal nerve. Syncope episodes disappeared after operation.

摘要

迷走神经副神经节瘤是神经内分泌系统的罕见肿瘤之一。我们报告一例具有该疾病罕见特征的迷走神经副神经节瘤病例:心搏停止和晕厥。晕厥发作发生在该疾病主要症状出现前3年。由于存在血管减压成分,双腔起搏器未能预防晕厥发作。该患者通过肿瘤及迷走神经整块切除获得成功治疗。术后晕厥发作消失。

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