Park Hyeon-Jin, Jeong Dong-Ho, Song Hyung-Geun, Lee Geon-Kook, Han Gi-Seok, Cha Sang-Hoon, Ha Tae-Sun
Department of Pediatrics, Chungbuk National University Hospital, 62 Kaeshin- dong, Heungdok-gu, Cheongju, Chungbuk 361-711, Korea.
Yonsei Med J. 2003 Aug 30;44(4):740-3. doi: 10.3349/ymj.2003.44.4.740.
A myeloid sarcoma (MS) is an extramedullary tumor consisting of primitive granulocytic precursor cells. Although most such tumors have been reported in patients with acute myelogenous leukemia, MS is rarely recognized as an isolated tumor without any evidence of leukemia. However, in such cases, the initial diagnosis of MS can be difficult, so initial misdiagnosis rates of up to 75% have been reported. This report describes an unusual case of MS in a 3-year 5-month-old girl presenting as bilateral renal enlargements, and brain masses, with multiple bone involvements, but no hematological abnormalities.
髓系肉瘤（MS）是一种由原始粒细胞前体细胞组成的髓外肿瘤。虽然大多数此类肿瘤在急性髓系白血病患者中已有报道，但MS很少被认为是一种无白血病证据的孤立性肿瘤。然而，在这种情况下，MS的初始诊断可能很困难，因此据报道初始误诊率高达75%。本报告描述了一例罕见的MS病例，患者为一名3岁5个月大的女孩，表现为双侧肾脏肿大、脑肿块及多处骨骼受累，但无血液学异常。
