Memon Sattar A, Mandhan Parkash, Qureshi Javed Naeem, Shairani Asif Jamil
Liaquat University of Medical & Health Sciences, Jamshoro/Hyderabad, Pakistan.
Med Sci Monit. 2003 Sep;9(9):CS92-4.
Rapunzel syndrome is a rare condition and occurs when gastric trichobezoar extends beyond the pylorus into the bowel. Till to date, only thirteen such cases have been reported in literature in paediatric age group. We present an additional case and also report the first recurrence of the Rapunzel syndrome in a child.
Rapunzel syndrome in a 12-year-old girl is presented who also had the recurrence. The pathogenesis, clinical features, diagnosis, treatment and literature are reviewed briefly.
Recurrence of Rapunzel Syndrome is very uncommon, and does occur only if the patients are left untreated for their underlying problem. Therefore, to prevent this, a comprehensive management should always be considered.
长发公主综合征是一种罕见病症,当胃内毛石延伸至幽门之外进入肠道时就会发生。迄今为止,儿科年龄组仅有13例此类病例在文献中被报道。我们现报告一例新增病例,同时报道一名儿童首次出现长发公主综合征复发的情况。
报告一名12岁患有长发公主综合征复发的女孩。简要回顾了其发病机制、临床特征、诊断、治疗及相关文献。
长发公主综合征复发非常罕见,只有在患者潜在问题未得到治疗时才会发生。因此,为预防这种情况,应始终考虑进行全面管理。