May D, Rilliet B, Berney J
Clinique de neurochirurgie, Hôpital cantonal universitaire de Genève, Suisse.
Neurochirurgie. 1992;38(6):347-52.
Published cases of cervical dysraphic lesions are rare. Their estimated proportion is about 5% of the entire group of spinal dysraphism. Four cases are reported, representing 2 types of lesion: 2 meningoceles with a simple fibrous band fixing the posterior aspect of the cord to the skin and 2 meningomyelocystoceles with other associated anomalies (hydromyelia, hydrocephalus, Chiari II, Peter's ocular anomaly). The clinical presentation is that of a soft posterior cervical mass without marked neurological impairement. The surgical treatment is simple, consisting in the resection of the lesion, intradural exploration to untighten the cord if fixed by a fibrous band, and drainage of the hydrocephalus. Neurological outcome is generally good immediately but may need sometimes secondary surgical exploration.
已发表的颈椎神经管闭合不全性病变病例很少见。据估计，它们在整个脊柱神经管闭合不全组中所占比例约为5%。本文报告了4例病例，代表2种病变类型：2例为脑膜膨出，有一条简单的纤维带将脊髓后部固定于皮肤；2例为脊髓脊膜囊肿并伴有其他相关异常（脊髓积水、脑积水、Chiari II型畸形、彼得氏眼部异常）。临床表现为颈部后方有一柔软肿块，无明显神经功能损害。手术治疗简单，包括切除病变、进行硬脊膜内探查以松解被纤维带固定的脊髓，以及引流脑积水。神经功能预后一般在术后即刻良好，但有时可能需要二次手术探查。
