Kasliwal M K, Dwarakanath S, Mahapatra A K
Department of Neurosurgery, All India Institute of Medical Sciences, New Delhi 110029, India.
Childs Nerv Syst. 2007 Nov;23(11):1291-3. doi: 10.1007/s00381-007-0387-5. Epub 2007 Jul 13.
Cervical myelomeningoceles (CMMC) are a less common but distinct subgroup of myelomeningoceles. Their embryology and clinical characteristics vary from the more common thoracolumbar variant. Only a few small series have been published addressing this lesion in the literature with the largest one of them addressing nine patients. The authors present one of the largest series of cervical myelomeningoceles, review their embryology, clinical features, and their management strategies.
This study included all the children who were managed for cervical myelomeningocele between Jan 2001 to July 2006 at our center.
There were a total of ten children (five boys and five girls) operated on for cervical myelomeningoceles. The ages ranged between 2 months to 14 months. Neurological examination was normal in majority of the children with absence of gross orthopedic deformity in all the children. Three patients had associated hydrocephalus, two had Chiari malformation, and four of them had a syrinx. Surgical excision of the sac was performed for all.
Cystic dysraphisms of the cervical differ embryologically, clinically, and structurally from thoracolumbar meningomyelocele and have a more favorable outcome. A good pre operative evaluation is recommended to assess any associated anomalies and identify the internal structures. Surgery excision of these lesions with intradural exploration of the sac to release any potential adhesion bands as well as other associated anomalies is recommended.
颈髓脊膜膨出(CMMC)是一种较罕见但独特的脊髓脊膜膨出亚组。它们的胚胎学和临床特征与更常见的胸腰段脊髓脊膜膨出不同。文献中仅有少数关于该病变的小系列报道,其中最大的系列报道了9例患者。本文作者呈现了最大系列之一的颈髓脊膜膨出病例,回顾了其胚胎学、临床特征及治疗策略。
本研究纳入了2001年1月至2006年7月在我们中心接受颈髓脊膜膨出治疗的所有儿童。
共有10名儿童(5名男孩和5名女孩)接受了颈髓脊膜膨出手术。年龄范围在2个月至14个月之间。大多数儿童神经检查正常,所有儿童均无明显的骨科畸形。3例患者合并脑积水,2例有Chiari畸形,其中4例有脊髓空洞症。所有患者均进行了囊肿切除术。
颈段囊性神经管闭合不全在胚胎学、临床和结构上与胸腰段脊膜脊髓膨出不同,且预后更佳。建议进行全面的术前评估,以评估任何相关异常并识别内部结构。建议对这些病变进行手术切除,并对囊肿进行硬膜内探查,以松解任何潜在的粘连带以及其他相关异常。