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与支气管扩张相关的系统性超敏性血管炎。

Systemic hypersensitivity vasculitis associated with bronchiectasis.

作者信息

Tanaka E, Tada K, Amitani R, Kuze F

机构信息

Department of Infection and Inflammation, First Clinic of Medicine, Kyoto University, Japan.

出版信息

Chest. 1992 Aug;102(2):647-9. doi: 10.1378/chest.102.2.647.

Abstract

Systemic hypersensitivity vasculitis developed in a 53-year-old man during acute exacerbation of bronchiectasis infected with Pseudomonas aeruginosa. High grade fever, mononeuropathy multiplex, cutaneous vasculitis, and biopsy specimen-proved mesangioproliferative glomerulonephritis with crescent formation and leukocytoclastic vasculitis associated with circulating immune complex occurred. Corticosteroid and cyclophosphamide therapy was effective for vasculitis and bronchiectasis.

摘要

一名53岁男性在支气管扩张症急性加重期感染铜绿假单胞菌后发生了系统性超敏性血管炎。出现了高热、多发性单神经病、皮肤血管炎,活检标本证实为伴有新月体形成的系膜增生性肾小球肾炎以及与循环免疫复合物相关的白细胞破碎性血管炎。皮质类固醇和环磷酰胺治疗对血管炎和支气管扩张症有效。

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