van Heereveld H A, van den Hoogen F H, de Vaan G, Blok W L, de Coo I F, Boerbooms A M
Afd. Interne Geneeskunde, Academisch Ziekenhuis St. Radboud, Nijmegen.
Ned Tijdschr Geneeskd. 1992 Sep 26;136(39):1917-9.
Primary antiphospholipid syndrome or PAPS is characterised by antiphospholipid antibodies and arterial and/or venous thromboses. Numerous other clinical features have been shown to be related to this syndrome. Chorea is a well known but rare phenomenon in systemic lupus erythematosus; it has been shown to be strongly related to the presence of antiphospholipid antibodies. We describe two patients with chorea that appeared to be caused by the PAPS.
原发性抗磷脂综合征(PAPS)的特征是存在抗磷脂抗体以及动脉和/或静脉血栓形成。许多其他临床特征也已被证明与该综合征有关。舞蹈症是系统性红斑狼疮中一种广为人知但罕见的现象;已证明它与抗磷脂抗体的存在密切相关。我们描述了两名似乎由原发性抗磷脂综合征引起舞蹈症的患者。