Vieco P T, del Carpio-O'Donovan R, Melanson D, Montes J, O'Gorman A M, Meagher-Villemure K
Department of Diagnostic Radiology, Montreal Neurological Hospital, Quebec, Canada.
Pediatr Radiol. 1992;22(5):366-9. doi: 10.1007/BF02016259.
Dysplastic gangliocytoma (Lhermitte-Duclos disease) is a rare entity. Usually presenting as a posterior fossa mass, dysplastic gangliocytoma is not a true neoplasm but a hard-to-characterize lesion that may represent an abnormality of cell migration or a phacomatosis. Previous reports of CT findings are rare in the radiologic literature, and high-field (1.5 Tesla) MR images have never been described in the pediatric age group. We present a case of dysplastic gangliocytoma in a one-year-old boy with CT and MR findings.
发育异常性神经节细胞瘤(Lhermitte-Duclos病)是一种罕见的疾病。发育异常性神经节细胞瘤通常表现为后颅窝肿块,它并非真正的肿瘤,而是一种难以定性的病变,可能代表细胞迁移异常或错构瘤。以往关于CT表现的报道在放射学文献中较为罕见,且儿科年龄组的高场强(1.5特斯拉)磁共振图像从未被描述过。我们报告一例1岁男孩发育异常性神经节细胞瘤的CT和磁共振表现。