Zhdanov V S, Chazova I E, Veselova S P, Mareev V Iu, Lobova N M
Ter Arkh. 1992;64(3):112-6.
The authors relate the results of a clinical and post mortem examination of 12 patients who died for primary pulmonary hypertension (PPH). The clinical, x-ray, echocardiography and electrocardiography data were of the same type in all the patients. Macroscopic studies of the heart also demonstrated similar changes: the heart mass was increased because of hypertrophy of its right parts. At the same time the microscopic picture of small vessels of the lungs turned out fairly diverse. Based on these differences all the cases were divided into 3 groups: veno-occlusive disease, recurrent pulmonary thromboembolism, plexogenic pulmonary arteriopathy. However, certain differences were noted inside the groups either. It is therefore assumed that PPH is a collective notion, uniting different alterations in small pulmonary vessels, that lead to a considerable rise of pressure in the pulmonary artery.
作者阐述了对12例死于原发性肺动脉高压（PPH）患者的临床及尸检结果。所有患者的临床、X线、超声心动图及心电图数据类型相同。心脏的宏观研究也显示出相似的变化：由于右心部分肥厚，心脏重量增加。同时，肺部小血管的微观图像差异较大。基于这些差异，所有病例被分为3组：静脉闭塞性疾病、复发性肺血栓栓塞、丛状肺血管病。然而，组内也存在一些差异。因此可以认为，PPH是一个综合概念，涵盖了导致肺动脉压力显著升高的肺小血管的不同病变。
