Hoppen T, Jacobi G, Rister M
Klinik für Kinder- und Jugendmedizin, Städtisches Klinikum Kemperhof, Koblenz.
Klin Padiatr. 2003 Sep-Oct;215(5):268-9. doi: 10.1055/s-2003-42671.
Subacute sclerosing panencephalitis is a rare progressive neurological disorder of childhood and early adolescence caused by persistent measles virus. The diagnosis is based upon characteristic clinical manifestations, periodic EEG discharges, raised antibody titre against measles/SSPE in the plasma and cerebrospinal fluid and increase of gamma-globulins in the cerebrospinal fluid. Histopathological examination shows neuronal loss, astrogliosis, demyelination, infiltration of inflammatory cells, and intranuclear inclusions in neurons, oligodendrocytes and astrocytes. In most cases nucleocapsids are detected by electron microscopy. Although treatment is still undetermined, combination of intrathecal high-dose interferon-alpha and intravenous ribavirin administered at an early stage of SSPE seems to be effective.
亚急性硬化性全脑炎是一种由持续性麻疹病毒引起的儿童和青少年早期罕见的进行性神经疾病。诊断基于特征性临床表现、脑电图周期性放电、血浆和脑脊液中抗麻疹/亚急性硬化性全脑炎抗体滴度升高以及脑脊液中γ-球蛋白增加。组织病理学检查显示神经元丢失、星形胶质细胞增生、脱髓鞘、炎症细胞浸润以及神经元、少突胶质细胞和星形胶质细胞中的核内包涵体。在大多数情况下,通过电子显微镜可检测到核衣壳。尽管治疗方法仍未确定,但在亚急性硬化性全脑炎早期鞘内注射高剂量α干扰素和静脉注射利巴韦林联合使用似乎有效。