Jenkins P C, Flanagan M F, Jenkins K J, Sargent J D, Canter C E, Chinnock R E, Vincent R N, O'Connor G T
Department of Pediatrics, Dartmouth Medical School, Hanover, NH 03755, USA.
Pediatr Cardiol. 2004 Jan-Feb;25(1):3-10. doi: 10.1007/s00246-003-0471-x. Epub 2003 Oct 13.
We sought to document morbidities and growth for patients with hypoplastic left heart syndrome (HLHS) to inform the initial surgical decision and understand healthcare needs. Data were obtained on 137 patients with HLHS, born between 1989 and 1994, who survived staged surgery ( n = 62) or transplantation ( n = 75) and had follow-up information available from four pediatric cardiac surgical centers. In patients with HLHS older than 1 year of age at follow-up, 93% experienced at least one major postsurgical morbidity. Morbidities depended on the surgery received. Hypertension, renal compromise, and abnormal infections were more common in transplanted patients than staged surgery patients. Staged surgery patients used more anticongestive medications and experienced more morbidities requiring interventional catheterization than did transplanted patients. Rejection was common for transplanted patients. On average these children spent 23 days per year in the hospital. Patients with HLHS were small for their age; 43% of staged surgery patients weighed below the third percentile at last information, compared to 19% of transplanted patients ( p = 0.003). The median height percentile was the 10th in both groups. Normal activity level was reported in more transplanted patients (90%) than staged surgery patients (49%; p < 0.001). Trade-offs between mortality and morbidity outcomes can help inform the initial surgical decision.
我们试图记录左心发育不全综合征(HLHS)患者的发病率和生长情况,为初始手术决策提供依据,并了解其医疗保健需求。我们获取了1989年至1994年出生的137例HLHS患者的数据,这些患者接受了分期手术(n = 62)或移植手术(n = 75)并存活下来,且有来自四个儿科心脏外科中心的随访信息。在随访时年龄超过1岁的HLHS患者中,93%至少经历过一种主要的术后发病情况。发病情况取决于所接受的手术。与接受分期手术的患者相比,高血压、肾功能损害和异常感染在接受移植手术的患者中更为常见。接受分期手术的患者使用更多的抗充血药物,且比接受移植手术的患者经历更多需要介入导管治疗的发病情况。移植排斥反应在接受移植手术的患者中很常见。这些儿童平均每年住院23天。HLHS患者的身高低于同龄人;在最后一次记录时,43%接受分期手术的患者体重低于第三百分位,而接受移植手术的患者这一比例为19%(p = 0.003)。两组患者的身高百分位中位数均为第10位。报告正常活动水平的接受移植手术的患者(90%)多于接受分期手术的患者(49%;p < 0.001)。死亡率和发病率结果之间的权衡有助于为初始手术决策提供依据。