Kiran Penukonda Sasi, Sowdi Vasantha Prema, Shetty Sumanth B, Venugopal U, Parameshwariah S, Dias Edwin, Kamala C S
Department of Pediatrics, K.S. Hegde Medical Academy, Deralakatte, Mangalore, India.
Indian J Pediatr. 2003 Sep;70(9):759-60. doi: 10.1007/BF02724322.
Sinus histiocytosis with massive lymphadenopathy is a rare histiocytic disorder with very few case reports in Indian literature. Immunological abnormalities have been documented in few cases. We report one such case of a child presenting with generalized lymphadenopathy and complicated by autoimmune hemolytic anemia, suggestive of an associated immune dysfunction.
伴巨大淋巴结病的窦性组织细胞增多症是一种罕见的组织细胞疾病，印度文献中的病例报告极少。少数病例记录了免疫异常情况。我们报告了这样一例患儿，其表现为全身淋巴结病，并并发自身免疫性溶血性贫血，提示存在相关的免疫功能障碍。
