Bánki J H, Meiners L C, Barentsz J O, Witkamp T D
University Hospital, Utrecht, The Netherlands.
Int J Card Imaging. 1992;8(4):249-54. doi: 10.1007/BF01146023.
Marfan's syndrome is a connective tissue disorder, which mainly affects the cardiovascular system, together with ocular, skeletal and connective tissue. The cardiovascular manifestations in particular determine the mortality of this disorder. We studied 13 patients, suffering of Marfan's syndrome, with suspected aortic dilatation by means of magnetic resonance imaging (MRI). Aneurysmal dilatation of the aortic root and dissection were the two major findings in our study. Two of the five patients with dissections presented without relevant symptoms in the medical history nor at the time of the MRI examination.
马凡氏综合征是一种结缔组织疾病，主要影响心血管系统，以及眼部、骨骼和结缔组织。心血管表现尤其决定了这种疾病的死亡率。我们通过磁共振成像（MRI）研究了13例疑似主动脉扩张的马凡氏综合征患者。主动脉根部瘤样扩张和夹层是我们研究中的两个主要发现。五例夹层患者中有两例在病史中及MRI检查时均无相关症状。
