Kersting-Sommerhoff B A, Sechtem U P, Schiller N B, Lipton M J, Higgins C B
J Comput Assist Tomogr. 1987 Jul-Aug;11(4):633-9. doi: 10.1097/00004728-198707000-00016.
A characteristic shape of the ascending aorta has been reported in patients with Marfan syndrome. To evaluate the capability of magnetic resonance (MR) imaging to distinguish between marfanoid and other aortic aneurysms, 11 Marfan patients (group 1), eight patients with ascending aorta enlargement (group 2), and 20 normal subjects (group 3) had transverse and sagittal MR of the thoracic aorta. Aortic diameter was measured at the sinuses of Valsalva (SV), the caudal portion of the ascending aorta, the prearch region (PA), the middle arch, and the descending aorta. The ratio SV/PA was significantly greater (p less than 0.001) in group 1 compared with groups 2 and 3. The SV/PA in all Marfan patients exceeded 1.4 but was less than 1.3 in subjects of groups 2 and 3. Magnetic resonance imaging provides definitive measurements of aortic dimensions and is potentially the method of choice for establishing the diagnosis of aortic involvement in Marfan syndrome and monitoring the course of aortic enlargement.
据报道，马方综合征患者升主动脉有特征性形态。为评估磁共振（MR）成像区分类马方综合征和其他主动脉瘤的能力，对11例马方综合征患者（第1组）、8例升主动脉扩张患者（第2组）和20名正常受试者（第3组）进行了胸主动脉的横断位和矢状位MR检查。在主动脉瓣窦（SV）、升主动脉尾部、弓前区（PA）、主动脉弓中部和降主动脉测量主动脉直径。与第2组和第3组相比，第1组的SV/PA比值显著更高（p<0.001）。所有马方综合征患者的SV/PA均超过1.4，而第2组和第3组受试者的该比值小于1.3。磁共振成像可对主动脉尺寸进行确切测量，可能是诊断马方综合征主动脉受累及监测主动脉扩张进程的首选方法。
