Curgunlu A, Karter Y, Tüfekci I B, Tunckale A, Karahasanoglu T
Department of Internal Medicine, Cerrahpasa Medical Faculty, Istanbul University, Istanbul, Turkey.
Clin Exp Rheumatol. 2003 Jul-Aug;21(4 Suppl 30):S41-3.
Benign cystic mesothelioma (BCM) is a rare neoplasm of the peritoneum, consisting of solitary or multiple cysts arising from mesothelial cells. Here we report a patient with a previous diagnosis of familial Mediterranean fever (FMF) presenting with abdominal distension and ascites which were found to be due to BCM. The co-existence of these two entities has not been reported previously. Ascites as the presenting feature of BMC is also a rare observation.
良性囊性间皮瘤(BCM)是一种罕见的腹膜肿瘤,由间皮细胞产生的单个或多个囊肿组成。在此,我们报告一例先前诊断为家族性地中海热(FMF)的患者,其表现为腹胀和腹水,经检查发现是由BCM所致。此前尚未有这两种疾病并存的报道。腹水作为BCM的首发症状也较为罕见。