成人多脾综合征伴多种内脏异常：胚胎学与临床考量

Polysplenia syndrome with various visceral anomalies in an adult: embryological and clinical considerations.

作者信息

Muneta S, Sakai S, Fukuda H, Imamura Y, Matsumoto I

机构信息

Department of Internal Medicine, Matsuyama Red Cross Hospital, Ehime, Japan.

出版信息

Intern Med. 1992 Aug;31(8):1026-31. doi: 10.2169/internalmedicine.31.1026.

DOI:10.2169/internalmedicine.31.1026

PMID:1477462

Abstract

A 26-year-old female with polysplenia syndrome is reported. She had numerous visceral anomalies including polysplenia, a short pancreas, a preduodenal portal vein, malrotation of the bowel, azygos continuation of the inferior vena cava, bilateral hyparterial bronchi and symmetrical liver lobation. Embryological and clinical considerations of polysplenia syndrome are described.

摘要

报告了一名患有多脾综合征的26岁女性。她有许多内脏异常，包括多脾、短胰腺、十二指肠前门静脉、肠旋转不良、下腔静脉奇静脉延续、双侧动脉下支气管和肝脏分叶对称。文中描述了多脾综合征的胚胎学和临床相关情况。