成人中检测到伴有十二指肠前门静脉的多脾综合征。
Polysplenia syndrome with preduodenal portal vein detected in adults.
作者信息
Seo Hyung-Il, Jeon Tae Yong, Sim Mun Sup, Kim Suk
机构信息
Department of Surgery, Postgraduate School of Medicine and Medical Research Institute, Pusan National University, Busan 602-739, South Korea.
出版信息
World J Gastroenterol. 2008 Nov 7;14(41):6418-20. doi: 10.3748/wjg.14.6418.
Abstract
Polysplenia syndrome, defined as the presence of multiple spleens of almost equal volume, is a rare condition involving congenital anomalies in multiple organ systems. We report this anomaly in a 41-year-old female who underwent a left lateral sectionectomy due to recurrent cholangitis and impacted left lateral duct stones. Polysplenia syndrome with preduodenal vein was diagnosed preoperatively by computed tomography (CT) and surgery was done safely. Although the polysplenia syndrome with preduodenal portal vein (PDPV) in adult is rarely encountered, surgeons need to understand the course of the portal vein and exercise caution in approaching the biliary tract.
摘要
多脾综合征定义为存在多个体积几乎相等的脾脏，是一种涉及多器官系统先天性异常的罕见病症。我们报告了一名41岁女性的这一异常情况，该患者因复发性胆管炎和左外侧胆管结石接受了左外侧肝段切除术。术前通过计算机断层扫描（CT）诊断为伴有十二指肠前静脉的多脾综合征，并安全地进行了手术。尽管成人中伴有十二指肠前门静脉（PDPV）的多脾综合征很少见，但外科医生需要了解门静脉的走行，并在处理胆道时谨慎操作。
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