[One-staged repair for coarctation of the aorta and annuloaortic ectasia with severe aortic regurgitation in a patient with Turner syndrome].

A 27-year-old woman with Turner syndrome was admitted to NCVC for congestive heart failure. 2-D echocardiography and magnetic resonance imaging (MRI) disclosed annuloaortic ectasia with severe aortic regurgitation and coarctation of the aorta. One staged operation by a modified Bentall procedure and extra-anatomical bypass grafting from the ascending aorta to the infrarenal abdominal aorta was successfully performed. The postoperative course was uneventful. The pressure gradient between upper and lower extremities decreased as to be 30 mmHg compared with preoperative 60 mmHg.