一名患有Swyer综合征的患者发生无性细胞瘤的肠道侵犯。

Intestinal invasion by a dysgerminoma in a patient with Swyer syndrome.

作者信息

Parker M, Barnhill D, Teneriello M, O'Connor D, Park R

机构信息

Department of Obstetrics and Gynecology, Walter Reed Army Medical Center, Washington, DC.

出版信息

Obstet Gynecol. 1992 Sep;80(3 Pt 2):567-9.

PMID:1495740

Abstract

An unusual case is presented of advanced dysgerminoma in a patient with Swyer syndrome, 46,XY pure gonadal dysgenesis. Unexpected regional invasion necessitated bowel resection, total abdominal hysterectomy, and bilateral salpingogonadectomy for a complete en bloc excision of the primary tumor mass and the dysgenetic gonads. This report illustrates the possible need for extensive operative resection in patients with Swyer syndrome.

摘要

本文报告一例罕见病例，患者为患有斯维尔综合征（46,XY单纯性腺发育不全）的晚期无性细胞瘤。因意外出现局部侵犯，需行肠切除术、全腹子宫切除术及双侧输卵管卵巢切除术，以完整整块切除原发性肿瘤团块及发育异常的性腺。本报告说明了斯维尔综合征患者可能需要进行广泛的手术切除。