Taberkant M, Chtata H, Lekehal B, Alaoui M, Sefiani Y, Boughroum A, Mahi O, El Mesnaoui A, Benjelloun A, Ammar F, Bensaid Y
Service de chirurgie vasculaire (Pr Y. BENSAID), Hôpital Avicenne, Rabat, Maroc.
J Mal Vasc. 2003 Dec;28(5):265-8.
Behçet's disease is an uncommon systemic process generally developing during the third or fourth decade of life. Recurrent inflammatory lesions are characteristic. Cardiovascular involvement, which may be arterial or venous, is rare but with particularly severe prognosis. Four cases of abdominal aortic aneurysm are reported. One patient underwent emergency surgery for acute rupture. All patients were male, age range 29-45 years, mean age 36.5 years. Three patients were followed for Behçet's disease. Surgical revascularization was performed in all four patients, mainly with prosthetic grafts, one with patch aortoplasty. The postoperative period was complicated by paraplegia and thrombosis of the prosthetic graft in the patient who underwent emergency surgery. On the basis of these cases and cases reported in the literature, it can be concluded that morbidity and mortality are high because of the etiology underlying vascular involvement in Behçet's disease.
白塞病是一种不常见的全身性疾病,通常在人生的第三或第四个十年发病。复发性炎症性病变是其特征。心血管受累情况,可能是动脉或静脉受累,较为罕见,但预后特别严重。本文报告了4例腹主动脉瘤病例。1例患者因急性破裂接受了急诊手术。所有患者均为男性,年龄范围29 - 45岁,平均年龄36.5岁。3例患者患有白塞病并接受了随访。所有4例患者均进行了手术血运重建,主要采用人工血管移植,1例采用补片主动脉成形术。接受急诊手术的患者术后出现了截瘫和人工血管血栓形成等并发症。基于这些病例以及文献中报道的病例,可以得出结论,由于白塞病血管受累的潜在病因,其发病率和死亡率都很高。