Marzban Mehrab, Mandegar Mohammad Hossein, Karimi Abbasali, Abbasi Kyomars, Movahedi Namvar, Navabi Mohammad Ali, Abbasi Seyed Hesameddin, Moshtaghi Naghmeh
Tehran Heart Center, Medical Sciences, University of Tehran, Tehran, Iran.
J Card Surg. 2008 Nov-Dec;23(6):765-8. doi: 10.1111/j.1540-8191.2008.00607.x.
Behcet's disease is a multisystem disorder and classified as "vasculitic syndrome with a wide variety of clinical manifestations." Cardiac involvement is very rare but can occur with different presentations including: pericarditis, cardiomyopathy, endocarditis, endomyocardial fibrosis, intracavitary thrombosis, and coronary artery disease. Great vessel involvement is more common. Recurrent Phlebitis, commonly involving large vessels (superior vena cava, inferior vena cava, hepatic veins) and cerebral veins are the sole presentation in this regard. Arterial involvement is expressed by aneurysm or pseudoaneurysmal formation. Due to the wide variety of cardiovascular manifestations and the resulting high mortality, cardiac surgeons should be familiar with this disease. In this paper we review the articles and introduce our four cases presenting with aneurysm of ascending aorta with free aortic insufficiency, aneurysm of descending aorta, pulmonary artery aneurysm, and pseudoaneurysm of aortic arch.
白塞病是一种多系统疾病，被归类为“具有多种临床表现的血管炎综合征”。心脏受累非常罕见，但可出现不同表现，包括：心包炎、心肌病、心内膜炎、心内膜心肌纤维化、心腔内血栓形成和冠状动脉疾病。大血管受累更为常见。复发性静脉炎，通常累及大血管（上腔静脉、下腔静脉、肝静脉）和脑静脉是这方面的唯一表现。动脉受累表现为动脉瘤或假性动脉瘤形成。由于心血管表现多种多样且导致高死亡率，心脏外科医生应熟悉这种疾病。在本文中，我们回顾了相关文章，并介绍了我们的4例病例，分别为升主动脉瘤合并主动脉瓣关闭不全、降主动脉瘤、肺动脉瘤和主动脉弓假性动脉瘤。
