[集合管（贝氏管）癌]
[Collecting duct (Bellini) carcinoma].
作者信息
de Pablo Cárdenas Alvaro, Pinós Paul Miguel Angel, Jiménez Aristu Javier Ignacio, Jiménez Calvo Jesús Manuel, Lozano Uruñuela Francico, Rivas Alonso Andrés, Santiago González de Garibay Andrés María, Guarch Troyas Rosa
机构信息
Servicio de Urología, Hospital Virgen del Camino, Pamplona, Navarra, España.
出版信息
Arch Esp Urol. 2004 Mar;57(2):153-6.
OBJECTIVES
To report one case of collecting duct (Bellini) carcinoma and to review the national bibliography. To analyze the clinical, diagnostic, and therapeutic features of this malignant renal tumor.
METHODS/RESULTS: A 36-year-old male presenting with monosymptomatic hematuria and clot retention was diagnosed of left renal mass suggestive of renal carcinoma. Radical nephrectomy with interaortocaval lymphadenectomy through an "L" abdominal incision (inverted Makuuchi) and postoperative radiotherapy were carried out. The pathologic report showed a collecting duct (Bellini) carcinoma. The patient died 34 months after surgery, having been treated with two courses of chemotherapy and palliative vertebral radiotherapy.
CONCLUSIONS
The collecting duct (Bellini) carcinoma is an infrequent malignant renal tumor. It does not differ from the clear cell adenocarcinoma either clinically or epidemiologically. However, it presents its own embryological, pathologic, immunohistochemical, and cytogenetic characteristics. Radical nephrectomy is the treatment of choice. Prognosis is ominous because of the aggressive behaviour and diagnosis in advanced stages.
目的
报告一例集合管（贝氏管）癌病例并回顾国内相关文献。分析这种恶性肾肿瘤的临床、诊断及治疗特征。
方法/结果：一名36岁男性因单纯性血尿和血凝块潴留就诊，被诊断为左肾肿物，提示肾癌。通过“L”形腹部切口（改良马氏切口）行根治性肾切除术及主动脉腔静脉间淋巴结清扫术，并进行术后放疗。病理报告显示为集合管（贝氏管）癌。该患者术后34个月死亡，期间接受了两个疗程的化疗及姑息性椎体放疗。
结论
集合管（贝氏管）癌是一种罕见的恶性肾肿瘤。在临床和流行病学方面与透明细胞腺癌并无差异。然而，它具有自身的胚胎学、病理学、免疫组织化学及细胞遗传学特征。根治性肾切除术是首选治疗方法。由于其侵袭性生物学行为及晚期诊断，预后不佳。
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