Kim K-J, Jang B-W, Lee S-K, Kim B-K, Nam S-L
Department of Obstetrics and Gynecology, Konyang University College of Medicine, Daejeon, Korea.
Int J Gynecol Cancer. 2004 Mar-Apr;14(2):370-2. doi: 10.1111/j.1048-891X.2004.014224.x.
Peripheral primitive neuroectodermal tumor (PNET) belongs to the PNET/Ewing's sarcoma family. PNET is a small round cell tumor of putative neuroectoderm origin and is the second most common sarcoma among children and young adults. It may occur anywhere in the body and within any age group; however, it is most likely to occur in the bone and soft tissues. There have been a small number of case reports of PNET arising in the ovary. We presented a case of PNET arising in the right ovary of an 18-year-old woman. The tumor was metastased to the lymph nodes of the pelvis and para-aorta at surgical staging. We had persecuted Taxol/carboplatin chemotherapy, pelvic cavity radiotherapy, and Vincristine/Actinomycin, Cyclophosphamide/Doxorubicin (VACA). She died after 10 months due to septic shock.
外周原始神经外胚层肿瘤（PNET）属于PNET/尤因肉瘤家族。PNET是一种推测起源于神经外胚层的小圆细胞肿瘤，是儿童和青年中第二常见的肉瘤。它可发生于身体的任何部位及任何年龄组；然而，最常发生于骨骼和软组织。卵巢发生PNET的病例报告较少。我们报告了一例发生于一名18岁女性右卵巢的PNET。手术分期时肿瘤已转移至盆腔和腹主动脉旁淋巴结。我们进行了紫杉醇/卡铂化疗、盆腔放疗以及长春新碱/放线菌素、环磷酰胺/阿霉素（VACA）化疗。她在10个月后因感染性休克死亡。
