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食管闭锁与胆道闭锁:一种罕见的关联。

Oesophageal atresia and biliary atresia: a rare association.

作者信息

Samujh R, Srinivasa Rao M, Mahajan J K, Bhattacharjee A, Rao K L N

机构信息

Department of Paediatric Surgery, Postgraduate Institute of Medical Education and Research, 160 012 Chandigarh, India.

出版信息

Pediatr Surg Int. 2004 Jun;20(6):467-8. doi: 10.1007/s00383-004-1178-7. Epub 2004 Apr 17.

DOI:10.1007/s00383-004-1178-7
PMID:15095104
Abstract

Oesophageal atresia is known to be associated with cardiovascular, gastrointestinal, genitourinary and skeletal anomalies. Its association with biliary atresia is very rare and only a few cases have been reported in the literature. Although biliary atresia could be part of a multiple anomaly syndrome, its isolated occurrence is even rare. We present a case of oesophageal atresia associated with biliary atresia.

摘要

已知食管闭锁与心血管、胃肠道、泌尿生殖系统及骨骼异常有关。其与胆道闭锁的关联非常罕见,文献中仅报道了少数病例。尽管胆道闭锁可能是多重异常综合征的一部分,但其单独出现更为罕见。我们报告一例食管闭锁合并胆道闭锁的病例。

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1
Oesophageal atresia and biliary atresia: a rare association.食管闭锁与胆道闭锁:一种罕见的关联。
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引用本文的文献

1
A study of associated congenital anomalies with biliary atresia.一项关于胆道闭锁相关先天性异常的研究。
J Indian Assoc Pediatr Surg. 2016 Jan-Mar;21(1):10-3. doi: 10.4103/0971-9261.158095.

本文引用的文献

1
Some observations on esophageal atresias and tracheoesophageal fistulas of congenital origin.
J Thorac Surg. 1957 Aug;34(2):141-72.
2
Combined pure esophageal atresia, duodenal atresia, biliary atresia, and pancreatic ductal atresia: prenatal diagnostic features and review of the literature.合并单纯食管闭锁、十二指肠闭锁、胆道闭锁和胰腺导管闭锁:产前诊断特征及文献复习
J Pediatr Surg. 2000 May;35(5):745-7. doi: 10.1053/jpsu.2000.6049.
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Association of oesophageal atresia and cholecystohepatic duct.食管闭锁与胆囊肝管的关联
Pediatr Surg Int. 1999;15(1):21-3. doi: 10.1007/s003830050503.
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