Lee Jong Heun, Soung Young Hwa, Lee Jong Woo, Park Won Sang, Kim Su Young, Cho Yong Gu, Kim Chang Jae, Seo Si Hyung, Kim Hong Sug, Nam Suk Woo, Yoo Nam Jin, Lee Sug Hyung, Lee Jung Young
Department of Pathology, College of Medicine, The Catholic University of Korea, Seoul 137-701, Korea.
J Pathol. 2004 Apr;202(4):439-45. doi: 10.1002/path.1532.
There is evidence that deregulation of apoptosis is mechanistically involved in cancer development and somatic mutations of apoptosis-related genes have been reported in human cancers. BID, a pro-apoptotic member of the Bcl-2 family, interconnects the extrinsic apoptosis pathway initiated by death receptors to the intrinsic apoptosis pathway. To explore the possibility that genetic alterations of BID might be involved in the development of human cancers, this study analysed the entire coding region and all splice sites in the human BID gene in 67 advanced gastric carcinomas. Overall, four BID mutations (6.0%) were detected that consisted of one frameshift and three missense mutations. The tumour-derived BID mutants were expressed in 293T cells and it was found that, compared with wild-type BID, the frequency of apoptosis was significantly reduced in cells expressing the gene containing the frameshift mutation. Furthermore, expression of the inactivating frameshift mutant interfered with cell death by overexpression of death receptors, indicating that this mutant inhibits the extrinsic apoptosis pathway in a dominant-negative fashion. Also, the frameshift mutation rendered cancer cells resistant to apoptosis induced by the anti-cancer drug 5-fluorouracil (5-FU). This is the first report of BID gene mutation in human malignancy. The data suggest that such mutations occur rarely in gastric cancers and that only a small fraction of BID mutations may lead to the loss of its apoptotic function.
有证据表明,细胞凋亡失调在机制上与癌症发展相关,并且在人类癌症中已报道了凋亡相关基因的体细胞突变。BID是Bcl-2家族的促凋亡成员,它将死亡受体启动的外源性凋亡途径与内源性凋亡途径相互连接。为了探究BID基因改变可能参与人类癌症发展的可能性,本研究分析了67例进展期胃癌中人类BID基因的整个编码区和所有剪接位点。总体而言,检测到4个BID突变(6.0%),包括1个移码突变和3个错义突变。将肿瘤来源的BID突变体在293T细胞中表达,发现与野生型BID相比,表达含有移码突变基因的细胞中凋亡频率显著降低。此外,失活的移码突变体的表达通过死亡受体的过表达干扰细胞死亡,表明该突变体以显性负性方式抑制外源性凋亡途径。而且,移码突变使癌细胞对抗癌药物5-氟尿嘧啶(5-FU)诱导的凋亡产生抗性。这是人类恶性肿瘤中BID基因突变的首次报道。数据表明,此类突变在胃癌中很少发生,并且只有一小部分BID突变可能导致其凋亡功能丧失。